Acetylcarnitine | decanoyl-L-carnitine |
propionyl-L-carnitine | lauroyl-L-carnitine |
butyryl-L-carnitine | myristoyl-L-carnitine |
isobutyril-L-carnitine | palmitoyl-L-carnitine |
valeryl-L-carnitine | Stearoyl-L-carnitine |
isovaleryl-L-carnitine | oleoyl-L-carnitine |
hexanoyl-L-carnitine | linoleoyl-L-carnitine |
octanoyl-L-carnitine |
Acyl-carnitine profiling is a common diagnostic test used for the diagnosis of inherited error of metabolism (mainly disorders of fatty acid oxidation that result to organic acidemias). Concentrations of carnitines are altered in primary disorders of the carnitine cycle and in disturbances of carnitine metabolism due to various biochemical disorders.